Case Reports

Primary pulmonary leiomyosarcoma: a rare malignant lung tumor

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Received: 16 April 2025
Published: 24 July 2025
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Primary Pulmonary Leiomyosarcoma (PPL) is an extremely rare malignant tumor. It has been reported that PPL may originate from the smooth muscle of the pulmonary parenchyma, pulmonary arteries, or bronchi. Patients with PPL may be asymptomatic or present with symptoms similar to those observed in other primary lung tumors.

This study reports the case of a 61-year-old man who presented with cough and hemoptysis as his primary complaints. Imaging revealed a lung mass, and the patient underwent cryobiopsy. He was subsequently diagnosed with PPL.

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Primary pulmonary leiomyosarcoma: a rare malignant lung tumor. (2025). Chest Disease Reports, 13(1). https://doi.org/10.4081/cdr.13.13898