SPLIT-APPENDIX TECHNIQUE: SURGICAL CHOICE FOR COMPLETE INCONTINENCE IN CAUDAL REGRESSION SYNDROME


Submitted: 18 April 2014
Accepted: 18 April 2014
Published: 31 December 2013
Abstract Views: 825
PDF: 739
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Authors

  • E. Cerchia The Section of Pediatric Surgery, Department of Medical Sciences, Surgery and neuroscience, University of Siena, Siena, Italy.
  • A.L. Bulotta The Section of Pediatric Surgery, Department of Medical Sciences, Surgery and neuroscience, University of Siena, Siena, Italy.
  • M. Ruscelli The Section of Pediatric Surgery, Department of Medical Sciences, Surgery and neuroscience, University of Siena, Siena, Italy.
  • R. Angotti The Section of Pediatric Surgery, Department of Medical Sciences, Surgery and neuroscience, University of Siena, Siena, Italy.
  • G. Di Maggio The Section of Pediatric Surgery, Department of Medical Sciences, Surgery and neuroscience, University of Siena, Siena, Italy.
  • M. Messina The Section of Pediatric Surgery, Department of Medical Sciences, Surgery and neuroscience, University of Siena, Siena, Italy.
In the last decades the surgery for total continent reconstruction has been changed by the introduction of intermittent catheterized stoma with the purpose to preserve urinary tract function, urinary continence, elimination of fecal soiling, preservation of quality of life with complete self-sufficiency. We report a rare case of complete incontinence in caudal regression syndrome in whom the appendix was long enough to be divided for creation of both channels for the treatment of urinary and fecal incontinence. A 9-year-old male patient with complete incontinence in caudal regression syndrome was submitted to a Mitrofanoff appendicovesicostomy procedure (AV) in conjunction with appendicocecostomy procedure (ACE). The appendix was divided into two different parts preserving adequate perfusion. Fecal continence was achieved for a period of 18-20 hours after a colonic irrigation with 500 ml of saline solution one time daily, while urinary continence was obtained after suburethral endoscopic injection of dextranomer/hyaluronic acid (Deflux) and intermittent catheterization every 3 hours with an evident reduction of upper urinary tract dilatation. The combination of ACE and Mitrofanoff principle have revolutionized the management of urinary and fecal incontinence in patients who are unable to utilize their urethra to keep themselves dry.

Cerchia, E., Bulotta, A., Ruscelli, M., Angotti, R., Di Maggio, G., & Messina, M. (2013). SPLIT-APPENDIX TECHNIQUE: SURGICAL CHOICE FOR COMPLETE INCONTINENCE IN CAUDAL REGRESSION SYNDROME. Journal of the Siena Academy of Sciences, 5(1), 93–97. https://doi.org/10.4081/jsas.2013.3840

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